Bệnh rỗng tủy

Syringomyelia is a condition where a fluid‑filled pocket (called a syrinx) forms inside the spinal cord and can slowly expand, stretching and damaging the nearby nerve pathways. It often develops with other problems such as Chiari malformation, past spinal injury, tumors, or scarring around the spinal cord.


1) What is this condition?

  • A syrinx is a tube‑ or bubble‑like cavity filled with spinal fluid that develops within the spinal cord, usually in the neck or upper back region.

  • As it grows, it can damage nerve fibers that control pain and temperature sensation, strength, and coordination.

  • Symptoms may include burning or stabbing pain, loss of temperature feeling in the shoulders/arms, hand weakness and clumsiness, stiffness, and sometimes scoliosis or bladder/bowel issues.


2) How serious is it?

  • Some people have a syrinx found on MRI with no symptoms; these may stay stable for years and only need monitoring.

  • When the syrinx enlarges or is already large, it can slowly cause permanent spinal cord damage and disability if not treated.

  • The condition usually worsens slowly over months to years; once nerve cells are badly damaged, full recovery is unlikely.


3) Non‑surgical treatments

  • “Watch and wait” with regular neurologic exams and MRI scans when symptoms are mild or absent.

  • Pain management: nerve‑pain medicines, standard painkillers, and sometimes specialist pain programs.

  • Physical and occupational therapy to address stiffness, posture, balance, arm/hand function, and to teach safe movement strategies.

  • Avoiding heavy straining, extreme neck/back stress, or activities that clearly worsen symptoms.


4) Types of surgery that may be necessary

  • Surgery to fix the underlying blockage of spinal fluid flow:

    • For Chiari malformation: posterior fossa decompression (opening space at the back of the skull and top of the spine).

    • For tumors, scar bands, or severe curvature: removing the mass or scar or correcting deformity.

  • Direct syrinx drainage with a small tube (shunt):

    • Syringo‑subarachnoid, syringo‑pleural, or syringo‑peritoneal shunts to drain fluid from inside the cord to another fluid space.


5) Goals of surgery vs non‑surgical care

  • Non‑surgical goals:

    • Avoid surgery when the syrinx is stable and symptoms are mild, while catching any worsening early by regular follow‑up.

    • Reduce pain, maintain strength and function, and adapt activities to protect the cord.

  • Surgery goals:

    • Restore normal spinal fluid flow around the cord and/or drain the syrinx to stop or slow further cord damage.

    • Stabilize or improve symptoms such as pain, weakness, and walking problems, knowing long‑standing damage may not fully reverse.


6) How surgery can “fix” the problem

  • Decompression for Chiari or scarring removes bone and tight coverings or scar tissue so spinal fluid can circulate freely outside the cord instead of being forced inside it.

  • Once outside flow is restored, the syrinx often shrinks or at least stops growing, reducing pressure on nerve tissue.

  • A shunt drains fluid directly from the syrinx to another space (around the cord, chest, or abdomen), lowering pressure inside the cord.


7) Risks of surgery (general and specific)

  • General risks: infection, bleeding, spinal fluid leak, blood clots, and anesthesia complications.

  • Decompression‑specific:

    • New or worse weakness, numbness, imbalance, or swallowing problems if the cord or nearby structures are injured.

    • Incomplete decompression or new scarring, so the syrinx persists or returns.

  • Shunt‑specific:

    • Shunt blockage, movement, breakage, or infection, sometimes needing repeat surgeries.


8) Chances this surgery will work

  • For Chiari‑related syringomyelia, decompression improves or stabilizes symptoms in about 70–80% or more of patients in many series.

  • Decompression often leads to partial or major shrinkage of the syrinx on MRI in most patients over months.

  • Shunt procedures show good short‑term relief in roughly 70–75% of cases but can have more long‑term failures or need for revisions, so they are often reserved for cases that do not respond to decompression.


9) Possible complications from the surgery

  • Persistent or recurrent syrinx requiring further surgery (for example, repeat decompression or shunt placement).

  • Worsening neurologic function, though major permanent worsening is uncommon in experienced hands.

  • With shunts: serious complications such as spinal deformity, chronic infection, or permanent weakness reported in a minority of patients.


10) Typical recovery from the condition

  • Without effective treatment, many syrinxes slowly enlarge, leading to progressive weakness, loss of temperature/pain sensation, hand dysfunction, and sometimes scoliosis or bladder/bowel issues.

  • Some people with small, stable syrinxes have little or no change over many years under regular monitoring.

  • Pain and functional limits can often be improved with long‑term therapy, pain management, and adaptive strategies, even when some nerve damage is permanent.


11) Typical recovery after surgery

  • Hospital stay is usually a few days, with neck/back soreness, fatigue, and activity limits for several weeks.

  • Symptom improvement can be gradual; many studies note months before clear gains, with syrinx shrinkage often seen over 3–12 months.

  • Physical and occupational therapy help rebuild strength, coordination, and safe movement patterns.


12) How long in the hospital

  • Standard posterior fossa decompression or spinal decompression/shunt surgeries often require about 3–5 days in hospital if there are no complications.

  • Longer stays may be needed if pre‑existing disability is significant or if spinal fluid leaks, infections, or combined procedures occur.


13) Long‑term outlook

  • Syringomyelia is chronic; even after successful surgery, long‑term follow‑up is needed because syrinxes can recur or new problems can appear.

  • Many people enjoy long‑term stabilization or improvement after decompression, with favorable outcomes reported in roughly 70–80% of surgical cases.

  • Post‑traumatic syringomyelia and long‑standing large syrinxes can be harder to control and may continue to cause slow decline despite treatment.


14) Need for outpatient follow‑up

  • Regular visits with neurology and neurosurgery for neurologic exams and periodic MRI scans to watch syrinx size and spinal cord health.

  • Ongoing rehab and pain‑management follow‑up to adjust exercise programs, braces, and medicines as needs change.

  • Monitoring for breathing issues in high (neck) syringomyelia and for late complications like new weakness, scoliosis, or bladder/bowel changes.